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Dernières publications
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Valentina Taglietti, Kaouthar Kefi, Lea Rivera, Oriane Bergiers, Nastasia Cardone, et al.. Thyroid-stimulating hormone receptor signaling restores skeletal muscle stem cell regeneration in rats with muscular dystrophy. Science Translational Medicine, 2023, 15 (685), ⟨10.1126/scitranslmed.add5275⟩. ⟨hal-04150315⟩
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A. Morin, Amalia Stantzou, Olga N. Petrova, John C.W. Hildyard, T. Tensorer, et al.. Dystrophin myonuclear domain restoration governs treatment efficacy in dystrophic muscle. Proceedings of the National Academy of Sciences of the United States of America, 2023, 120 (2), ⟨10.1073/pnas.2206324120⟩. ⟨hal-04122777⟩
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Chiffres clés
55
Publications avec texte intégral
Open Access
76 %
Mots clés
CTNNB1
Molecular Sequence Data
Duchenne muscular dystrophy DMD
Hear
CD38
Cardiomyopathy
Becker muscular dystrophy BMD
Invivo
Skeletal muscle
Activin Receptors
Dystrophie Musculaire de Duchenne DMD
MES
Morphogenesis
Mdx mouse
CaVβs
Duchenne muscular dystrophy
CaVβ1
Mice
Long noncoding RNA
Energy Metabolism/drug effects
Inhibitors
Cell homeostasis
Metabolism
DMO
Homeostasis
Antisense oligonucleotides
Becker Muscular Dystrophy
Knockout
Dystrophie musculaire de Becker
Jonction neuromusculaire JNM
Cardiomyopathie
Base Sequence
Delivery
Drp1
Dilated Cardiomyopathy
Inbred C57BL
Duchenne DMD dystrophy
Inbred mdx
Multi resolution modeling
Connexins
Calcium Channels
Multi exon skipping
LncARN
Clinical trials
Muscle
Molecular docking
Gene expression
Allele‐specific silencing therapy
Dystrophine
Dystrophy
Gene Expression Regulation/drug effects
LncRNA
Cell Biology
Animals
Multiresolution modeling
Isoformes
Epigenetics
Génomique
Cell Line
Dystrophin-EGFP
Human Umbilical Vein Endothelial Cells
Diseases
Exon skipping
MiARN
Becker BMD muscular dystrophy
CaV subunits
Gene modifiers
DMD
Long QT
BMD
Isoforms
Mitochondrial fission
Liver
Ex-vivo
Dystrophie Musculaire de Becker BMD
Becker muscular dystrophy
LKB1
Heart Failure
Dystrophin
Adult muscle stem cells
Cultured
Modificateurs de gènes
DHPR α1S
Cells
Hepatocellular carcinoma
Dystrophin central domain
Immunoglobulin Fc Fragments/pharmacology
Genomic
Muscle Biology
Dystrophie myotonique de type 1 DM1
Dynamin 2
Animal/physiopathology
Centronuclear myopathy
Cachexia
Becker muscular dystrophy BMD Duchenne muscular dystrophy DMD miRNA nNOS
L-Type
Autophagy
Male
Humans
Calcium